Juvenile Dermatomyositis in Turkish Children
نویسندگان
چکیده
منابع مشابه
Juvenile dermatomyositis.
Juvenile dermatomyositis (JDMS) is a chronic inflammatory condition characterized by muscle weakness and a distinctive rash caused by underlying vasculopathy. Long-term complications include subcutaneous and muscular calcification, contractures and in some cases the gradual development of a second connective tissue disease. Early aggressive treatment with systemic immunosuppressants and other a...
متن کاملJuvenile dermatomyositis.
The clinical profile of 7 children and their follow-up is described. There was female preponderance with mate to female ratio of 1:6. The median age of onset was 6 years. All the patients had skin rash, muscle weakness and abnormal enzyme profile. Muscle biopsy was performed in 6 and was abnormal in all of them. The electromyogram (EMG) was performed in 6 and was found abnormal in five. All the...
متن کاملThe role of etanercept in juvenile dermatomyositis (JDMS) in children
Introduction Juvenile dermatomyositis is a rare autoimmune disease characterised by profound muscle weakness in addition to skin lesions, calcinosis, and underlying vasculopathy. Current treatment plans, including methotrexate and corticosteroids, are ineffective in some patients and may be associated with significant adverse events. The benefits and risks of etanercept in JDMS are not well stu...
متن کاملJuvenile Dermatomyositis in Pregnancy
Juvenile dermatomyositis has variable clinical presentations both in and outside of pregnancy. A literature review indicated that optimal maternal and fetal outcomes can be anticipated when the pregnancy is undertaken while the disease is in remission. Poorer outcomes are associated with flare-up of the disease in early pregnancy compared with exacerbation in the second or third trimester, when...
متن کاملCardiac findings in children with juvenile Dermatomyositis at disease presentation
BACKGROUND Juvenile Dermatomyositis (JDM) is a pediatric vasculopathy characterized primarily by skin and muscle involvement. Cardiac findings have been reported in children with JDM but have rarely been investigated in detail. METHODS We aimed to describe the relevant clinical and laboratory cardiac findings of a cohort of patients with JDM, followed at one centre, at disease diagnosis. RE...
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ژورنال
عنوان ژورنال: Turkish Journal of Rheumatology
سال: 2011
ISSN: 1309-0291,1309-0283
DOI: 10.5606/tjr.2011.036